A Significant Proportion of Children with Morphea En Coup De Sabre and Parry-Romberg Syndrome Have Neuroimaging Findings
نویسندگان
چکیده
منابع مشابه
Parry-Romberg Syndrome with En Coup de Sabre
Parry-Romberg syndrome (PRS) is a relatively rare degenerative disorder that is poorly understood. PRS is characterized by slowly progressing atrophy affecting one side of the face, and is frequently associated with localized scleroderma, especially linear scleroderma, which is known as en coup de sabre. This is a report of the author's experiences with PRS accompanying en coup de sabre, and a ...
متن کاملParry Romberg syndrome: a close differential diagnosis of linear scleroderma en coup de sabre.
This 45 years old lady complained of asymmetry of her face since the age of 15 years. She also complained of decreased sweating on the left side and an intermittent left hemicranial headache. Examination revealed marked atrophy of the left side of the face involving the skin, subcutaneous tissue and muscles of the orbital, maxillary and mandibular regions. There was no induration or tightening ...
متن کاملProgressive facial and cerebral hemiatrophy: Parry-Romberg syndrome or scleroderma "en coup de sabre"?
Acta Neurologica Taiwanica Vol 13 No 4 December 2004 From the Department of Neurology, Chang Gung Memorial Hospital, Linkou Medical Center, Taoyuan, Taiwan. Received November 19, 2004. Revised and Accepted November 29, 2004. Reprint requests and correspondence to: Nai-Shin Chu, MD. Department of Neurology, Chang Gung Memorial Hospital, No. 199, Tung-Hwa N. Road, Taipei, Taiwan. E-mail: chu060@c...
متن کاملMorphea “en coup de sabre”: An unusual oral presentation
Morphea, or localized scleroderma, is an inflammatory disease that leads to sclerosis of the skin and underlying tissues due to excessive collagen deposition. Oral involvement is unusual and it may produce white linear fibrotic areas with a scar-like appearance, atrophy of tongue papillae, gingival recession and alveolar bone resorption. We report a case of a 13-year-old girl who consulted for ...
متن کاملAtypical Neuroimaging Manifestations of Linear Scleroderma “en coup de sabre”
Linear scleroderma "en coup de sabre" is a subset of localized scleroderma with band-like sclerotic lesions typically involving the fronto-parietal regions of the scalp. Patients often present with neurologic symptoms. On imaging, patients may have lesions in the cerebrum ipsilateral to the scalp abnormality. Infratentorial lesions and other lesions not closely associated with the overlying sca...
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ژورنال
عنوان ژورنال: Pediatric Dermatology
سال: 2012
ISSN: 0736-8046
DOI: 10.1111/pde.12001